Chapter 32. Managing infants and children with auditory neuropathy spectrum disorder (ANSD)
Abstract
Key Points
1. ANSD is a heterogeneous disorder and has a number of potential sites-of-lesion depending on the underlying cause. Hence, the hearing configuration, speech perception, and functional and speech language outcomes are highly variable.
2. Specific assessment techniques need to be used to correctly diagnose ANSD using auditory brainstem response (ABR) testing.
3. Clinicians need to be aware of undiagnosed and late-onset ANSD
4. Cortical auditory evoked potentials (CAEPs) and assessments of functional auditory behaviour can assist with the decision to fit hearing aids and the evaluation of the effectiveness of amplification.